Table 1:
Signs and Symptoms of Cystic Fibrosis
Respiratory
Gastrointestinal
Genitourinary
Asthma Meconium ileus Absence of bilateral vas deferens
Bronchitis/
Chronic productive cough
Recurrent right lower-quadrant pain Male and female infertility
Pseudomonas aeruginosa/
Staphylococcal pneumonia
airway colonization

Distal intestinal
obstructive syndrome

Cervical plugging
Nasal polyps Biliary cirrhosis Female urinary incontinence
Pansinusitis Portal hypertension Recurrent vaginal yeast infections
Clubbing Fat-soluble vitamin deficiency
(vitamins A, D, E, or K)
 
  Recurrent pancreatitis
Diabetes
Failure to thrive
Adapted from Welsh MJ, Tsui L-C, Boat TF, et al. Cystic fibrosis. In: Scriver CR, Beaudet AL, Sly WS, et al, eds. The Metabolic and Molecular Basis of Inherited Disease. New York: McGraw-Hill, 1995:3801.
Copyright 2005 The Cleveland Clinic Foundation

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