Table 2:
Signs and Symptoms of Idiopathic Interstitial Pneumonias
Features
UIP/IPF
NSIP
BOOP
RB-ILD
DIP
LIP
Mean age (yr)
57
49
55
36
42
~50
Onset
Insidious
Subacute
Subacute
Insidious
Insidious
Insidious
Smoking associated?
Strongly increases risk
No
No
Required
Required
No
Mortality rate
70% (5yr)
11% (5yr)
Low
0%
27% (12yr)
30%?
Response to steroids?
No
Good
Good
Good
Good
Variable
Complete recovery?
No
Yes
Yes
Sometimes
Yes
Variable
  
Copyright 2002 The Cleveland Clinic Foundation

Return to Idiopathic Interstitial Lung Disease Chapter