Table 2:
Clinical Manifestations of Alpha1-antitrypsin Deficiency
Asymptomatic
Symptomatic
Children
Adults
Neonatal or infant hepatitis Chronic obstructive pulmonary disease
Prolonged cholestasis in infancy Chronic hepatitis
Hepatosplenomegaly Cirrhosis with or without
portal hypertension
Hepatocellular carcinoma
  
Copyright 2002 The Cleveland Clinic Foundation

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